Characterization and Clinical Management of Dilated Cardiomyopathy
Dilated cardiomyopathy (DCM) is a particular phenotype of non-ischemic systolic heart failure, frequently recognizing a genetic background and affecting relatively young patients with few comorbidities. Nowadays, long-term survival of DCM patients has been markedly improved due to an early diagnosis...
Saved in:
Sonstige: | |
---|---|
Year of Publication: | 2021 |
Language: | English |
Physical Description: | 1 electronic resource (232 p.) |
Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
id |
993545487904498 |
---|---|
ctrlnum |
(CKB)5400000000043722 (oapen)https://directory.doabooks.org/handle/20.500.12854/68283 (EXLCZ)995400000000043722 |
collection |
bib_alma |
record_format |
marc |
spelling |
Merlo, Marco edt Characterization and Clinical Management of Dilated Cardiomyopathy Basel, Switzerland MDPI - Multidisciplinary Digital Publishing Institute 2021 1 electronic resource (232 p.) text txt rdacontent computer c rdamedia online resource cr rdacarrier Dilated cardiomyopathy (DCM) is a particular phenotype of non-ischemic systolic heart failure, frequently recognizing a genetic background and affecting relatively young patients with few comorbidities. Nowadays, long-term survival of DCM patients has been markedly improved due to an early diagnosis and uninterrupted and tailored follow-up under constant optimal medical and non-pharmacological evidence-based treatments. Nevertheless, DCM is still one of the most common causes of heart transplantation in the western world. Clinical management requires an integrated and systematic use of diagnostic tools and a deeper investigation of the basic mechanisms underlying the disease. However, several emerging issues remain debated. Specifically, the genotype–phenotype correlation, the role of advanced imaging techniques and genetic testing, the lack of appropriate risk stratification models, the need for a multiparametric and multidisciplinary approach for device implantation, and a continuous reclassification of the disease during follow-up remain challenging issues in clinical practice. Therefore, the aim of this Special Issue is to shed the light on the most recent advancements in characterization and clinical management of DCM in order to unveil the conundrum of this particular disease. English Medicine bicssc SCN5A cardiac sodium channel cardiac channelopathy dilated cardiomyopathy precision medicine arrhythmias atrial fibrillation cardiomyopathy heart failure supraventricular arrhythmia systolic dysfunction tachycardiomyopathy ventricular arrhythmia left atrial strain cardiac resynchronization therapy muscular dystrophy calcium heart gene therapy phospholamban Serca2a mdx oxidative stress membrane stabilization left ventricular noncompaction congenital heart disease congestive heart failure non-ischemic cardiomyopathy genetics desmin mitochondrial dysfunction myopathy whole exome sequencing laminopathy LMNA biomarkers troponin T NT-proBNP malignant ventricular arrhythmia arrhythmic risk stratification DNA methylation alternative splicing epigenetics nonischemic dilated cardiomyopathy cardiac magnetic resonance imaging late gadolinium enhancement long axis strain left ventricle sphericity index major adverse cardiovascular events sex differences left ventricular reverse remodelling long-term outcomes left ventricle non-compaction cardiomyopathy cardiac magnetic resonance titin RNA binding motif protein 20 (RBM20) sarcomere diastolic dysfunction phosphorylation non-sense mRNA decay mammalian target of rapamycin (mTOR) complex-1 duchenne muscular distrophy 3-03943-761-5 3-03943-762-3 Merlo, Marco oth |
language |
English |
format |
eBook |
author2 |
Merlo, Marco |
author_facet |
Merlo, Marco |
author2_variant |
m m mm |
author2_role |
Sonstige |
title |
Characterization and Clinical Management of Dilated Cardiomyopathy |
spellingShingle |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_full |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_fullStr |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_full_unstemmed |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_auth |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_new |
Characterization and Clinical Management of Dilated Cardiomyopathy |
title_sort |
characterization and clinical management of dilated cardiomyopathy |
publisher |
MDPI - Multidisciplinary Digital Publishing Institute |
publishDate |
2021 |
physical |
1 electronic resource (232 p.) |
isbn |
3-03943-761-5 3-03943-762-3 |
illustrated |
Not Illustrated |
work_keys_str_mv |
AT merlomarco characterizationandclinicalmanagementofdilatedcardiomyopathy |
status_str |
n |
ids_txt_mv |
(CKB)5400000000043722 (oapen)https://directory.doabooks.org/handle/20.500.12854/68283 (EXLCZ)995400000000043722 |
carrierType_str_mv |
cr |
is_hierarchy_title |
Characterization and Clinical Management of Dilated Cardiomyopathy |
author2_original_writing_str_mv |
noLinkedField |
_version_ |
1787548718259503105 |
fullrecord |
<?xml version="1.0" encoding="UTF-8"?><collection xmlns="http://www.loc.gov/MARC21/slim"><record><leader>04480nam-a2201033z--4500</leader><controlfield tag="001">993545487904498</controlfield><controlfield tag="005">20231214133445.0</controlfield><controlfield tag="006">m o d </controlfield><controlfield tag="007">cr|mn|---annan</controlfield><controlfield tag="008">202105s2021 xx |||||o ||| 0|eng d</controlfield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(CKB)5400000000043722</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(oapen)https://directory.doabooks.org/handle/20.500.12854/68283</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(EXLCZ)995400000000043722</subfield></datafield><datafield tag="041" ind1="0" ind2=" "><subfield code="a">eng</subfield></datafield><datafield tag="100" ind1="1" ind2=" "><subfield code="a">Merlo, Marco</subfield><subfield code="4">edt</subfield></datafield><datafield tag="245" ind1="1" ind2="0"><subfield code="a">Characterization and Clinical Management of Dilated Cardiomyopathy</subfield></datafield><datafield tag="260" ind1=" " ind2=" "><subfield code="a">Basel, Switzerland</subfield><subfield code="b">MDPI - Multidisciplinary Digital Publishing Institute</subfield><subfield code="c">2021</subfield></datafield><datafield tag="300" ind1=" " ind2=" "><subfield code="a">1 electronic resource (232 p.)</subfield></datafield><datafield tag="336" ind1=" " ind2=" "><subfield code="a">text</subfield><subfield code="b">txt</subfield><subfield code="2">rdacontent</subfield></datafield><datafield tag="337" ind1=" " ind2=" "><subfield code="a">computer</subfield><subfield code="b">c</subfield><subfield code="2">rdamedia</subfield></datafield><datafield tag="338" ind1=" " ind2=" "><subfield code="a">online resource</subfield><subfield code="b">cr</subfield><subfield code="2">rdacarrier</subfield></datafield><datafield tag="520" ind1=" " ind2=" "><subfield code="a">Dilated cardiomyopathy (DCM) is a particular phenotype of non-ischemic systolic heart failure, frequently recognizing a genetic background and affecting relatively young patients with few comorbidities. Nowadays, long-term survival of DCM patients has been markedly improved due to an early diagnosis and uninterrupted and tailored follow-up under constant optimal medical and non-pharmacological evidence-based treatments. Nevertheless, DCM is still one of the most common causes of heart transplantation in the western world. Clinical management requires an integrated and systematic use of diagnostic tools and a deeper investigation of the basic mechanisms underlying the disease. However, several emerging issues remain debated. Specifically, the genotype–phenotype correlation, the role of advanced imaging techniques and genetic testing, the lack of appropriate risk stratification models, the need for a multiparametric and multidisciplinary approach for device implantation, and a continuous reclassification of the disease during follow-up remain challenging issues in clinical practice. Therefore, the aim of this Special Issue is to shed the light on the most recent advancements in characterization and clinical management of DCM in order to unveil the conundrum of this particular disease.</subfield></datafield><datafield tag="546" ind1=" " ind2=" "><subfield code="a">English</subfield></datafield><datafield tag="650" ind1=" " ind2="7"><subfield code="a">Medicine</subfield><subfield code="2">bicssc</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">SCN5A</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiac sodium channel</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiac channelopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">dilated cardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">precision medicine</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">arrhythmias</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">atrial fibrillation</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">heart failure</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">supraventricular arrhythmia</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">systolic dysfunction</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">tachycardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">ventricular arrhythmia</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">left atrial strain</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiac resynchronization therapy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">muscular dystrophy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">calcium</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">heart</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">gene therapy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">phospholamban</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">Serca2a</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">mdx</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">oxidative stress</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">membrane stabilization</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">left ventricular noncompaction</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">congenital heart disease</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">congestive heart failure</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">non-ischemic cardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">genetics</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">desmin</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">mitochondrial dysfunction</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">myopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">whole exome sequencing</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">laminopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">LMNA</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">biomarkers</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">troponin T</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">NT-proBNP</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">malignant ventricular arrhythmia</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">arrhythmic risk stratification</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">DNA methylation</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">alternative splicing</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">epigenetics</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">nonischemic dilated cardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiac magnetic resonance imaging</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">late gadolinium enhancement</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">long axis strain</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">left ventricle sphericity index</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">major adverse cardiovascular events</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">sex differences</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">left ventricular reverse remodelling</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">long-term outcomes</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">left ventricle non-compaction cardiomyopathy</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">cardiac magnetic resonance</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">titin</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">RNA binding motif protein 20 (RBM20)</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">sarcomere</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">diastolic dysfunction</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">phosphorylation</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">non-sense mRNA decay</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">mammalian target of rapamycin (mTOR) complex-1</subfield></datafield><datafield tag="653" ind1=" " ind2=" "><subfield code="a">duchenne muscular distrophy</subfield></datafield><datafield tag="776" ind1=" " ind2=" "><subfield code="z">3-03943-761-5</subfield></datafield><datafield tag="776" ind1=" " ind2=" "><subfield code="z">3-03943-762-3</subfield></datafield><datafield tag="700" ind1="1" ind2=" "><subfield code="a">Merlo, Marco</subfield><subfield code="4">oth</subfield></datafield><datafield tag="906" ind1=" " ind2=" "><subfield code="a">BOOK</subfield></datafield><datafield tag="ADM" ind1=" " ind2=" "><subfield code="b">2023-12-15 05:54:36 Europe/Vienna</subfield><subfield code="f">system</subfield><subfield code="c">marc21</subfield><subfield code="a">2022-04-04 09:22:53 Europe/Vienna</subfield><subfield code="g">false</subfield></datafield><datafield tag="AVE" ind1=" " ind2=" "><subfield code="i">DOAB Directory of Open Access Books</subfield><subfield code="P">DOAB Directory of Open Access Books</subfield><subfield code="x">https://eu02.alma.exlibrisgroup.com/view/uresolver/43ACC_OEAW/openurl?u.ignore_date_coverage=true&portfolio_pid=5337928950004498&Force_direct=true</subfield><subfield code="Z">5337928950004498</subfield><subfield code="b">Available</subfield><subfield code="8">5337928950004498</subfield></datafield></record></collection> |